Leucine and glucose kinetics in glycogen storage disease type IIIa
J Inherit Metab Dis
.
1997 Nov;20(6):847.
doi: 10.1023/a:1005304809354.
Authors
O A Bodamer
1
,
E Mayatepek
,
J V Leonard
Affiliation
1
NMED unit, Institute of Child Health, London, UK.
PMID:
9427162
DOI:
10.1023/a:1005304809354
No abstract available
Publication types
Case Reports
MeSH terms
Child, Preschool
Glucose / biosynthesis
Glucose / metabolism*
Glycogen Storage Disease Type III / metabolism*
Humans
Kinetics
Leucine / metabolism*
Liver / metabolism
Male
Substances
Leucine
Glucose