Determination of total fatty acids in plasma: cis-5-tetradecenoic acid (C14:1 omega-9) in the diagnosis of long-chain fatty acid oxidation defects

J Inherit Metab Dis. 1999 May;22(3):286-8. doi: 10.1023/a:1005567030040.
No abstract available

MeSH terms

  • 3-Hydroxyacyl CoA Dehydrogenases / deficiency*
  • Acyl-CoA Dehydrogenase
  • Acyl-CoA Dehydrogenase, Long-Chain
  • Child
  • Fatty Acid Desaturases / deficiency*
  • Fatty Acids / blood
  • Fatty Acids, Monounsaturated / blood*
  • Humans
  • Lipid Metabolism, Inborn Errors / blood
  • Lipid Metabolism, Inborn Errors / diagnosis*
  • Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase

Substances

  • Fatty Acids
  • Fatty Acids, Monounsaturated
  • 3-Hydroxyacyl CoA Dehydrogenases
  • Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase
  • Fatty Acid Desaturases
  • Acyl-CoA Dehydrogenase
  • Acyl-CoA Dehydrogenase, Long-Chain