Erythromelalgia: Review of clinical characteristics and pathophysiology
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Cited by (69)
Erythromelalgia: A Review of Medical Management Options and Our Approach to Management
2023, Mayo Clinic ProceedingsCitation Excerpt :For patients with EM who do not have contraindications to aspirin, a daily 325-mg dose should be administered for at least 1 month. Aspirin is especially effective in patients who have secondary EM due to underlying myeloproliferative disease, such as essential thrombocytosis and polycythemia vera; dramatic improvement has been reported to occur within days of aspirin initiation.21,22 The antiplatelet effects of aspirin make it particularly useful in this subset of patients.
Aspirin and its pleiotropic application
2020, European Journal of PharmacologyCitation Excerpt :The dose of aspirin used ranges from 325 to 650 mg per day, with a 500 mg dose of aspirin lasting for 3 days. This long-lasting effect of aspirin can also be used in diagnostics for myeloproliferative disease-linked secondary erythromelalgia (Kurzrock and Cohen, 1991; Preston, 1983). Aspirin has also been suggested as a treatment in necrobiosis lipoidica diabeticorum - a rare skin condition associated with diabetes mellitus and characterized by degenerative and granulomatous changes (Reid et al., 2013).
Erythromelalgia
2013, Vascular Medicine: A Companion to Braunwald's Heart Disease: Second EditionPediatric erythromelalgia: A retrospective review of 32 cases evaluated at Mayo Clinic over a 37-year period
2012, Journal of the American Academy of DermatologyCitation Excerpt :The clinical presentation was consistent with that described in adult patients: during symptomatic periods, the affected areas were red, hot, and painful3; between these episodes, they were frequently cool, cyanotic, and mildly uncomfortable.15 Underlying disorders previously described in association with erythromelalgia2,3,5,16,17 were not present in this group of pediatric patients; in particular, none had myeloproliferative disease. Only one patient had hypertension.
Hurwitz Clinical Pediatric Dermatology, Fouth Edition
2011, Hurwitz Clinical Pediatric Dermatology, Fouth EditionThrombohemorrhagic complications of myeloproliferative disorders
2010, Blood ReviewsCitation Excerpt :Administration of aspirin or NSAID typically results in alleviation of the symptoms,30–32 though in some cases platelet-pheresis or cytoreduction is needed. Erythromelalgia, although not restricted to MPD,33 raises a high suspicion for an MPD, since it has never been observed in secondary thrombocytosis, suggesting that the major pathogenetic role for the phenomenon is associated with qualitative platelet abnormalities.34 Bleeding in MPD is less frequent and clinically grave than thrombosis, and it is more common in ET patients with high platelet counts.35