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History, anatomic forms, and pathogenesis of Chiari I malformations

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Abstract

Introduction

Chiari I malformations constitute a group of entities of congenital or acquired etiology that have in common descent of the cerebellar tonsils into the cervical spinal canal. In recent years, since the advent of magnetic resonance imaging, an increasing number of asymptomatic, doubtfully symptomatic, and minimally symptomatic patients with Chiari I malformations have been diagnosed. This has resulted in controversy about the multiple therapeutic strategies indicated for these problems.

Object

With the intention of updating the knowledge that we currently have on the Chiari I malformation and the related syringomyelia we review the literature and discuss the historical background, pathogenesis, anatomic forms, clinical presentation, and diagnostic procedures of these abnormalities.

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  1. Section of Neurosurgery, Hospital C. Durand, Buenos Aires, Argentina

    Edgardo Schijman

  2. Division of Neurosurgery, University of Buenos Aires School of Medicine, Av Libertador 2698 1-F, (1425), Buenos Aires, Argentina

    Edgardo Schijman

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Schijman, E. History, anatomic forms, and pathogenesis of Chiari I malformations. Childs Nerv Syst 20, 323–328 (2004). https://doi.org/10.1007/s00381-003-0878-y

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