Table 1

Baseline clinical characteristics

n (%)
Male gender50 (58)
Age, years (median (range))12.4 (0–18.4)
Weight, kg (median (range))38.6 (2–101)
Cardiac medications
 Beta-blockers91 (55)
 Disopyramide38 (23)
 Calcium channel blockers16 (10)
 Amiodarone10 (6)
Comorbidities (n)
 ENT
  OSA3
 Orthopaedic
  Scoliosis4
  Polyarthralgia1
 Respiratory
  Asthma4
 Congenital cardiac disease
  VSD1
  Aortic stenosis1
 Neurology
  Epilepsy1
  Autistic spectrum disorder3
  Developmental delay (acquired/congenital)3
  Hydrocephalus1
 Metabolic
  Diabetes mellitus2
 Renal
  Polycystic kidney1
  • Data expressed as number (%). Total number of patients is 86 unless otherwise stated.

  • ENT, ears, nose and throat; OSA, obstructive sleep apnoea; VSD, ventricular septal defect.