Table 1

Patient demographics and baseline clinical parameters

 Age13±3 years (range 6–18 years)
 Gender49% female
 Weight44.2±9.6 kg
 Height154±16 cm
 WHO class 2/351%/49 %
 Resting oxygen saturation91.1±10.9 %
Haemodynamic parameters
 Mean pulmonary arterial pressure60±21 mm Hg
 Pulmonary vascular resistance index17.0±9.4 WU/m2
 Pulmonary vascular resistance index after vasodilator testing (nitric oxide)14.5±8.4 WU/m2
 Mean right atrial pressure7.7±3.7 mm Hg