Table 1

Complications of varicella in children with inborn errors of metabolism

Inborn errors of metabolismNumberHistory of clinical varicellaMetabolic decompensation needing hospital admissionSecondary bacterial infection
Mitochondrial respiratory chain defect53292*5
Fatty acid oxidation disorder1310
Glycogen storage disorder921
Urea cycle disorder96
Glutaric aciduria851
Maple syrup urine disease60
Methylmalonic aciduria531
  • * One child admitted to intensive care with lactic acidosis.