| Presenting feature | Number (%) of cases (n = 55) |
| Significant neonatal respiratory distress | 37 (67) |
| Abnormal situs | 38 (69) |
| Cough most days | 46 (84) |
| Sputum production | 24 (44) |
| Rhinorrhoea from the newborn period | 42 (76) |
| Wheeze | 16 (29) |
| Sinusitis | 6 (11) |
| Serous otitis media | 28 (51) |
| Hearing loss | 14 (25) |
| Diagnosis made in a sibling | 6 (11) |
Modified from Coren et al.2 Most children had multiple symptoms, typically a combination of upper and lower airway disease.