Table 6

 Comparison of visual outcome in various paediatric series

First authorPatientsVisual loss at presentation*†Permanent visual loss*†
Severe visual loss defined as worse than 6/60 (or 20/200) loss in either eye.
*Defined as either decreased visual acuity or field defect.
†Percentage taken over total number of patients even when visual data not available.
‡Lessell reported a series with poor visual outcome.
Baker review of pre-1985 cases91852%
Baker, 1985103630%16%
3% severe
Couch, 198572416%8% severe loss
Lessell, 198585100%‡
40% severe
Babikian, 1992203020%3%
Cinciripini, 1998211060%10% severe
Phillips, 1998223540%19%
10 patients with optic
atrophy
Youroukos, 2000233628%6%
Salman, 2001243238%9%
3% severe
Kesler, 2002252762%0%