Table 2

 Neurology controls, clinical diagnosis (n = 100)

Patients denoted with * had positive ABGA Western immunoblotting.
Dystonic (n = 32)
    EncephalitisInvasive (n = 5) (HSV, EBV, VZV)
Inflammatory (n = 4) (Aicardi Goittieres and Coats disease)
Rasmussen’s encephalitis (n = 2)
SSPE (n = 1)
    VascularBasal ganglia stroke (n = 6)
Vasculitis (n = 1)
    MetabolicKernicterus, mitochondrial cytopathy, Batten’s disease, Lesch Nyhan, Sanfillipo, Glutaric aciduria type 1 (n = 1 each)
    OtherStatus dystonicus* (n = 2), nvCJD, basal ganglia tumour, athetoid cerebral palsy, drug induced rigidity, juvenile Parkinson’s (n = 1 each)
Encephalitis with no extrapyramidal features (n = 17)
    InvasiveUnidentified organism* (n = 12), HSV (n = 2), mycoplasma (n = 1), adenoviral (n = 1), neurocysticosis (n = 1)
Immune mediated CNS disorders (n = 45)
    Demyelinating disordersAcute disseminated encephalomyelitis (non-streptococcal) (n = 16)
Multiphasic disseminated encephalomyelitis (n = 2)
Multiple sclerosis (n = 4)
Optic neuritis (n = 3)
    “Autoimmune disorders”Rasmussen’s encephalitis (n = 1)
Rasmussen’s encephalitis (n = 1)
Dancing eyes syndrome (n = 9)
Post-infectious ataxia/cerebellitis* (n = 7)
CINCA (n = 3)
Other neurology controls (n = 6)
Epilepsy (n = 3), myasthenia gravis (n = 1), metachromatic leukodystrophy* (n = 1), Bell’s palsy (n = 1)