Clinical characteristics (n = 52)
Mean | Range | |
Age at initial evaluation (y) | 7.9 | 1.0–16 |
Age at most recent evaluation (y) | 15.5 | 3.0–28 |
Length of follow up (y) | 7.7 | 2.0–15 |
No. (%) | Male | |
Familial Marfan cases (%) | 33 (63) | 15 |
Sporadic Marfan cases (%) | 19 (37) | 10 |
Pectus deformity (%) | 35 (67) | 14 |
Excavatum (%) | 13 (25) | 8 |
Carinatum (%) | 22 (42) | 13 |
Scoliosis (%) | 23 (44) | 12 |
Ectopia lentis (%) | 32 (62) | 14 |