Table 1

Clinical characteristics (n = 52)

Mean Range
Age at initial evaluation (y) 7.91.0–16
Age at most recent evaluation (y)15.53.0–28
Length of follow up (y) 7.72.0–15
No. (%) Male
Familial Marfan cases (%)33 (63)15
Sporadic Marfan cases (%)19 (37)10
Pectus deformity (%)35 (67)14
 Excavatum (%)13 (25) 8
 Carinatum (%)22 (42)13
Scoliosis (%)23 (44)12
Ectopia lentis (%)32 (62)14