Table 3

Pulmonary function

Patient 1 2 3 4 5 6 Mean age
Age (y) 1st RFT5554544 years and 7 months
Age (y) last RFT8787767 years
Mean RFT
1st FVC74%55%50%88%47%75%65%
Last FVC66%59%57%80%59%99%70%
1st FEV1 79%37%37%66%49%85%59%
Last FEV1 63%34%30%76%46%82%55%
1st peak flow97%43%55%58%65%101%70%
Last peak flow66%34%36%62%51%85%56%
  • Values in per cent predicted for height.8

  • RFT, respiratory function test.