Characteristics of patients with osteogenesis imperfecta
Children | Adults | ||||||
---|---|---|---|---|---|---|---|
n | Male:female | Age (years) (mean (range)) | n | Male:female | Age (years) (mean (range)) | ||
Sillence type | |||||||
I | 13 | 8:5 | 9.6 (3.1–14.3) | 36 | 15:21 | 42.3 (18.6–63.5) | |
III | 10 | 8:2 | 11.5 (4.0–18.0) | 5 | 0:5 | 29.3 (21.9–37.2) | |
IV | 8 | 6:2 | 8.0 (5.0–12.0) | 14 | 5:9 | 31.3 (18.1–52.9) | |
Collagen defect | |||||||
Quantitative | 7 | 4:3 | 7.9 (3.1–15.7) | 18 | 9:9 | 39.3 (19.4–61.7) | |
Qualitative | 13 | 11:2 | 11.9 (4.0–18.0) | 15 | 4 / 11 | 32.1 (18.1–52.9) |