Table 1

Characteristics of patients with osteogenesis imperfecta

ChildrenAdults
nMale:femaleAge (years) (mean (range))nMale:femaleAge (years) (mean (range))
Sillence type
 I138:59.6 (3.1–14.3)3615:2142.3 (18.6–63.5)
 III108:211.5 (4.0–18.0)50:529.3 (21.9–37.2)
 IV86:28.0 (5.0–12.0)145:931.3 (18.1–52.9)
Collagen defect
 Quantitative74:37.9 (3.1–15.7)189:939.3 (19.4–61.7)
 Qualitative1311:211.9 (4.0–18.0)154 / 1132.1 (18.1–52.9)