Length of aganglionosis. Comparing lengths of aganglionosis between collected CCHS/Hirschprung cases, and the Sydney 30 year experience of Hirschprung’s disease alone, or with Down’s syndrome
| Length | CCHS/HSCR (n) | CCHS/HSCR (%) | Down’s syndrome/ HSCR (%) | All HSCR (non-CCHS, non-Down’s) (%) |
|---|---|---|---|---|
| Rectal | 4 | 10.2 | 7.5 | 10.9 |
| Sigmoid | 6 | 15.4 | 70.0 | 65.2 |
| Left colon | 2 | 5.1 | 12.5 | 12.2 |
| Rest of colon | 4 | 10.2 | 2.5 | 3.6 |
| TCA (+ ileal) | 18 | 46.2 | 5.0 | 6.5 |
| Mid-small bowel | 2 | 5.1 | 0 | 1.5 |
| Proximal small bowel | 3 | 7.7 | 0 | 0 |
| Total | 39 | 100 |
CCHS = congenital hypoventilation syndrome; HSCR = Hirschprung’s disease; TCA = total colonic aganglionosis.