TY - JOUR T1 - Respiratory complications of the rheumatological diseases in childhood JF - Archives of Disease in Childhood JO - Arch Dis Child SP - 752 LP - 758 DO - 10.1136/archdischild-2014-306049 VL - 101 IS - 8 AU - Anne E Richardson AU - Kishore Warrier AU - H Vyas Y1 - 2016/08/01 UR - http://adc.bmj.com/content/101/8/752.abstract N2 - Pleuropulmonary manifestations of rheumatological diseases are rare in children but pose a significant risk to overall morbidity and mortality. We have reviewed the literature to provide an overview of the respiratory complications of the commonest rheumatological diseases to occur in children (juvenile systemic lupus erythematosus, scleroderma, juvenile dermatomyositis, mixed connective tissue disease, granulomatosis with polyangitis and juvenile idiopathic arthritis). Pulmonary function testing in these patients can be used to refine the differential diagnosis and establish disease severity, but also has a role in ongoing monitoring for respiratory complications. Early detection of pulmonary involvement allows for prompt and targeted therapies to achieve the best outcome for the child. This is best achieved with joint specialist paediatric rheumatology and respiratory reviews in a multidisciplinary setting. ER -