PT  - JOURNAL ARTICLE
AU  - T O Crawford
AU  - R L Skolasky
AU  - R Fernandez
AU  - K J Rosquist
AU  - H M Lederman
TI  - Survival probability in ataxia telangiectasia
AID  - 10.1136/adc.2006.094268
DP  - 2006 Jul 01
TA  - Archives of Disease in Childhood
PG  - 610--611
VI  - 91
IP  - 7
4099  - http://adc.bmj.com/content/91/7/610.short
4100  - http://adc.bmj.com/content/91/7/610.full
SO  - Arch Dis Child2006 Jul 01; 91
AB  - Ataxia telangiectasia is a rare, multiorgan neurodegenerative disorder with enhanced vulnerability to cancer and infection. Median survival in two large cohorts of patients with this disease, one prospective and one retrospective, is 25 and 19 years, with a wide range. Life expectancy does not correlate well with severity of neurological impairment.