RT Journal Article
SR Electronic
T1 Superior vena cava thrombosis causing respiratory obstruction successfully resolved by stenting in a small bowel transplant candidate
JF Archives of Disease in Childhood
JO Arch Dis Child
FD BMJ Publishing Group Ltd and Royal College of Paediatrics and Child Health
SP 163
OP 164
DO 10.1136/adc.83.2.163
VO 83
IS 2
A1 Peters, M
A1 Beath, S V
A1 Puntis, J W L
A1 John, P
YR 2000
UL http://adc.bmj.com/content/83/2/163.abstract
AB A 4 year old child was referred for small bowel transplantation. He had superior vena cava obstruction secondary to numerous central venous line placements; alternative routes for long term central venous access were compromised by extensive venous occlusive disease. Patency for the superior vena cava was re-established with stenting, which allowed for radiological placement of another central venous line. Long term survival in infants and young children with intestinal failure is dependent on adequate central venous access for the administration of parenteral nutrition. Line sepsis and physical damage to the catheter often necessitates multiple central venous catheter placements during their early life and these children are at risk of catheter related veno-occlusive disease. Recurrent sepsis and the loss of satisfactory venous access for the administration of parenteral nutrition is life threatening and is an indication for intestinal transplantation in up to 41% of patients reported by the small bowel registry.