TY - JOUR T1 - Cystic fibrosis presenting as kwashiorkor with florid skin rash. JF - Archives of Disease in Childhood JO - Arch Dis Child SP - 446 LP - 448 DO - 10.1136/adc.69.4.446 VL - 69 IS - 4 AU - R J Phillips AU - C M Crock AU - M J Dillon AU - P T Clayton AU - A Curran AU - J I Harper Y1 - 1993/10/01 UR - http://adc.bmj.com/content/69/4/446.abstract N2 - Two infants with a florid erythematous rash and generalised oedema, hypoalbuminaemia, and anaemia were found to have cystic fibrosis. This rare presentation is associated with false negative sweat tests, delays in diagnosis, and a considerable mortality. It is proposed that this presentation represents a manifestation of kwashiorkor secondary to malabsorption. The recognition that these infants have kwashiorkor provides some insight into the pathogenesis and management of their illness. ER -