RT Journal Article
SR Electronic
T1 Chronic suppurative lung disease in sisters mimicking cystic fibrosis
JF Archives of Disease in Childhood
JO Arch Dis Child
FD BMJ Publishing Group Ltd and Royal College of Paediatrics and Child Health
SP 520
OP 524
DO 10.1136/adc.49.7.520
VO 49
IS 7
A1 Cogswell, J. J.
A1 Risdon, R. A.
A1 Taylor, Brent
YR 1974
UL http://adc.bmj.com/content/49/7/520.abstract
AB Two sisters are described with fatal chronic obstructive lung disease of unknown origin. The lung condition was clinically and histologically indistinguishable from cystic fibrosis and the salivary glands showed pathological changes expected in cystic fibrosis. Neither child had abnormal sweat electrolytes, they had no bowel symptoms, and the pancreas was normal at necropsy.