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Recent advances in the management of cystic fibrosis
  1. Jane C Davies1,2,
  2. Anne-Marie Ebdon2,
  3. Christopher Orchard3
  1. 1Imperial College, London, UK
  2. 2Royal Brompton and Harefield NHS Foundation Trust, London, UK
  3. 3Frimley Park Hospital, Frimley, Surrey, UK
  1. Correspondence to Professor Jane Davies, Imperial College, London, UK; Royal Brompton and Harefield NHS Foundation Trust, London SW3 6LR, UK; j.c.davies{at}


Cystic fibrosis is a disease that still causes a reduced life expectancy. The treatment burden remains high for affected individuals with often a combination of multiple oral and inhaled medications, as well as physiotherapy, required on a daily basis. In this article, we look at an overview of the pathogenesis, how this might lead to treatment options and look at some of the available new therapies, all in the aim of increasing life expectancy and reducing treatment burden.

  • Cystic Fibrosis
  • Therapeutics

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