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Cardiac disease and Rett syndrome


Rett syndrome (RS) is a neurodevelopmental disease,1 affecting approximately 1 in 10 000–15 000 females.2 Clinical severity of RS may vary with increasing age, following a four stage model.3

  • HRV, heart rate variability
  • RS, Rett syndrome
  • SD, sudden death
  • QT interval prolongation
  • Rett syndrome
  • cardiac arrhythmias
  • heart rate variability
  • sudden death

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