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Community child health, public health, and epidemiology
Respiratory management of the infant with type 1 spinal muscular atrophy
  1. A Bush1,
  2. J Fraser2,
  3. E Jardine3,
  4. J Paton3,
  5. A Simonds1,
  6. C Wallis4
  1. 1Royal Brompton Hospital, London, UK
  2. 2Paediatric Intensive Care Unit, Bristol Royal Hospital for Children, Bristol, UK
  3. 3Division of Developmental Medicine, University of Glasgow Royal Hospital for Sick Children, Glasgow, UK
  4. 4Great Ormond Street Hospital, London, UK
  1. Correspondence to:
    Prof A Bush
    Department of Paediatric Respiratory Medicine, Royal Brompton Hospital, Sydney Street, London SW3 6NP, UK; a.bushrbh.nthames.nhs.uk

Abstract

A recent paper has highlighted the differences in the respiratory management offered to infants with type 1 spinal muscular atrophy (SMA-1).1 Current views appear polarised between those who would offer nothing, to those who would proceed as far even as tracheostomy and long term invasive ventilation for these infants. Here we offer a personal view, as a possible template for managing a vexed and emotional problem. The complex non-respiratory aspects of the holistic care of these infants will not be discussed.

  • NIPPV, nasal intermittent positive pressure
  • SMA-1, type 1 spinal muscular atrophy
  • spinal muscular atrophy
  • non-invasive ventilation
  • cough
  • tracheostomy

https://doi.org/10.1136/adc.2004.065961

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    Footnotes

    • Competing interests: none declared