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Acute paediatrics
Treatment with cyclosporin A in a patient with Omenn’s syndrome
  1. A Meyer-Bahlburg1,
  2. J-P Haas3,
  3. R Haase1,
  4. U Eschrich1,
  5. A Wawer1,
  6. L Frank3,
  7. W Ch Marsch2,
  8. S Burdach1,
  9. G Horneff1
  1. 1Department of Pediatrics, Martin-Luther-University, School of Medicine, Halle/Saale, Germany
  2. 2Department of Dermatology and Venerology, Martin-Luther-University
  3. 3Children’s Hospital, Friedrich Alexander University Erlangen-Nürnberg, Germany
  1. Correspondence to:
    Dr A Meyer-Bahlburg, Department of Pediatrics, Martin-Luther-University, School of Medicine, Ernst-Grube-Str. 40, D-06120 Halle, Germany;
    almut.meyer-bahlburg{at}medizin.uni-halle.de

Abstract

Unless treated with haematopoetic stem cell transplantation, Omenn’s syndrome, a rare variant of severe combined immunodeficiency, is associated with a fatal outcome. We describe a male infant showing all the typical features of Omenn’s syndrome, who was successfully treated with cyclosporin A to improve clinical condition prior to haematopoetic stem cell transplantation.

  • cyclosporin A
  • Omenn’s syndrome
  • stem cell transplantation
  • CsA, cyclosporin A
  • SCT, stem cell transplantation

https://doi.org/10.1136/adc.87.3.231

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