Article Text
Acute paediatrics
Fatal Kawasaki disease caused by early occlusive coronary artery disease
Abstract
In Kawasaki disease severe coronary artery narrowing may develop at an early stage despite treatment with gammaglobulin and in the absence of prominent aneurysm formation or thrombosis. Vaso-occlusive disease may not be clinically or echocardiographically apparent until very severe.
- Kawasaki disease
- coronary artery occlusion
- coronary arteritis
- CRP, C reactive protein
- IVIG, intravenous gammaglobulin
- KD, Kawasaki disease
- LAD, left anterior descending