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Proteus syndrome and immunodeficiency
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- Published on: 15 March 2000
- Published on: 15 March 2000Lymphopenia in lymphatic malformationsShow More
Hodge et al(1) draw our attention to the possible association of hypogammaglobulinemia and global lymphopenia with Proteus syndrome. They suggest that this may be secondary to loss of immunoglobulins and lymphocytes into lymphoedematous tissue. We have seen a similar phenomenon in a child with massive cystic hygroma in the neck. Immunological investigations showed persistent severe lymphopenia with low levels of all lym...
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