Editor,—We read with interest this report of peripheral pulmonary artery stenosis in congenital generalised lipodystrophy but query the physical findings, particularly in case 1.¹ Furthermore, the term ‘pulmonary hypertension’ is used imprecisely. Pulmonary hypertension implies a pulmonary artery pressure higher than normal but whether this is systolic, diastolic, or mean has different connotations. The intensity of the pulmonary component of the second heart sound …