Article Text
Original article
Chronic bullous disease of childhood and a paecilomyces lung infection in chronic granulomatous disease
Abstract
A 12 year old boy suffering from p67-phoxdeficient chronic granulomatous disease presented with a bullous skin disease and a lung infection with paecilomyces species. The histopathology of a bullous lesion showed subepidermal blister formation and microabcesses containing eosinophils in the dermal papillae. By direct immunofluorescence, linear staining of IgA at the dermal-epidermal junction was detected which confirmed the clinical diagnosis of chronic bullous disease of childhood (linear IgA dermatosis)
- chronic granulomatous disease
- chronic bullous disease
- paecilomyces
- p67-phox