Article Text

Download PDFPDF

Cystic fibrosis presenting as kwashiorkor with florid skin rash.
  1. R J Phillips,
  2. C M Crock,
  3. M J Dillon,
  4. P T Clayton,
  5. A Curran,
  6. J I Harper
  1. Hospitals for Sick Children, London.


    Two infants with a florid erythematous rash and generalised oedema, hypoalbuminaemia, and anaemia were found to have cystic fibrosis. This rare presentation is associated with false negative sweat tests, delays in diagnosis, and a considerable mortality. It is proposed that this presentation represents a manifestation of kwashiorkor secondary to malabsorption. The recognition that these infants have kwashiorkor provides some insight into the pathogenesis and management of their illness.

    Statistics from

    Request Permissions

    If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. You will be able to get a quick price and instant permission to reuse the content in many different ways.