The relationship between the formation of urea and argininosuccinate in a patient with argininosuccinic aciduria studied with labelled precursors

Clin Sci Mol Med. 1974 Jun;46(6):715-27. doi: 10.1042/cs0460715.
No abstract available

MeSH terms

  • Adult
  • Amino Acid Metabolism, Inborn Errors / blood
  • Amino Acid Metabolism, Inborn Errors / metabolism*
  • Amino Acid Metabolism, Inborn Errors / urine
  • Arginine / biosynthesis
  • Arginine / metabolism
  • Arginine / urine*
  • Carbamates
  • Carbon Radioisotopes
  • Citrulline / blood
  • Citrulline / metabolism
  • Cystinuria / urine
  • Guanidines
  • Humans
  • Lyases / metabolism
  • Male
  • Middle Aged
  • Nitrogen Isotopes
  • Quaternary Ammonium Compounds / metabolism
  • Serum Globulins / metabolism
  • Succinates / biosynthesis
  • Succinates / urine*
  • Urea / biosynthesis*
  • Urea / urine

Substances

  • Carbamates
  • Carbon Radioisotopes
  • Guanidines
  • Nitrogen Isotopes
  • Quaternary Ammonium Compounds
  • Serum Globulins
  • Succinates
  • Citrulline
  • Urea
  • Arginine
  • Lyases