Table 2

Types of sickle cell disease

ConditionFreq.(%)
Hb SS853(64.8)
Hb SC366(27.8)
Hb S/β+ thalassaemia62(4.7)
Hb S/HPFH21(1.6)
Hb S/β°thalassaemia8(0.6)
Other sickle type diseases5(0.4)
Hb S/δβ thalassaemia<5
Total1317(100.0)
  • Figures are frequencies (column percentages). Other sickle type diseases include: Hb S/E, Hb S/Lepore and Hb S/Dpunjab. Percentages not shown for variants with frequency <5.