Inborn errors of metabolism | Number | History of clinical varicella | Metabolic decompensation needing hospital admission | Secondary bacterial infection |
---|---|---|---|---|
Mitochondrial respiratory chain defect | 53 | 29 | 2* | 5 |
Fatty acid oxidation disorder | 13 | 10 | ||
Glycogen storage disorder | 9 | 2 | 1 | |
Urea cycle disorder | 9 | 6 | ||
Glutaric aciduria | 8 | 5 | 1 | |
Mucopolysaccharidosis | 7 | 3 | ||
Maple syrup urine disease | 6 | 0 | ||
Methylmalonic aciduria | 5 | 3 | 1 | |
Others | 12 | 6 |
↵* One child admitted to intensive care with lactic acidosis.