Table 1

 Causes of explained sudden unexpected death in infancy

Cause of deathn (%)
MCAD, medium-chain acyl-CoA dehydrogenase deficiency.
Severe bronchopneumonia18 (35)
Generalised infection23 (45)
Vitium cordis4 (8)
Aspiration in combination with generalised infection2 (4)
Omphalocele1 (2)
MCAD1 (2)
Severe meningoencephalitis1 (2)
Dehydration1 (2)