Table 2

Clinical spectrum of Marfan’s syndrome

SiteCardinal featuresSymptomsEffects
JointsHypermobilityArthralgiaInstability
DislocationSoft tissue trauma
SkeletonMarfanoid habitusSlender extremities Pectus deformitiesScoliosis Arachnodactily
SkinHyperextensibilityThinning
Striae atrophicae
Papyraceous scars
Easy bruising
EyesEctopia lentisVisual problems
VasculatureAortic dilatationAneurysm
Mitral valveProlapseSBE
  • SBE, subacute bacterial endocarditis.