Table 2

Treatment and outcome in seven children with malignant androgen secreting adrenocortical tumours

PatientMetastasesTreatmentOutcome
4Local tumour growth, hepatic, and pulmonary metastases aao′p-DDD, vincristine cisplatin, etoposide,cyclophosphamide, carboplatin Alive 6 months pa
11Local tumour growth aao′p-DDD Died 5 months pa
12 Local tumour growth and hepatic metastases 3.8 years pao′p-DDD Died 4.3 years pa
16Hepatic and pulmonary metastases 9 months pa o′p-DDD, carboplatin, excision of pulmonary metastasesAlive 3.6 years pa
18 Hepatic and pulmonary metastases 10 months pao′p-DDDDied 1.8 years pa
19 Local tumour growth aa; pulmonary metastases 3.8 years paNone Alive 4.0 years pa
20Hepatic and pulmonary metastases 8 months pao′p-DDD Died 1.8 years pa
  • aa, at adrenalectomy; pa, postadrenalectomy; o′p-DDD, 1,1-dichloro-2-(o-chlorophenyl)-2-(p-chlorophenyl)-ethane.