Table 1

Characteristics of patients

Patient/Sex	Age (years)	Genotype	Shwachman score	FEV₁ (% predicted)	BMI SDS	Height SDS
1/F	9.1	2	90	83	−0.15	−1.40
2/F	12.3	1	85	67	0.18	0.70
3/F	11.0	1	90	93	−1.32	0.76
4/F	5.1	2	90	105	0.79	0.85
5/F	9.3	2	80	78	−0.98	−0.56
6/F	11.4	3	65	54	0.42	0.44
7/M	9.3	1	90	82	0.26	−0.20
8/M	7.6	2	90	103	−0.54	−1.20
9/M	7.9	1	75	100	0.31	−1.60
10/M	15.0	1	80	89	0.09	0.40
11/M	10.8	1	45	44	−1.64	−1.20
12/M	8.9	1	85	98	0.66	−0.58
13/M	12.5	2	65	31	−1.20	−1.75
14/M	8.2	1	90	87	−0.32	0.01
15/M	11.8	2	90	64	−1.48	−0.40
Mean	10.0		81	79	−0.33	−0.38
SD	2.4		13	22	0.81	0.90