Table 2

Clinical outcome

PatientDiabetes mellitusPancreatic enzyme supplementationCurrent medicationMental retardationGastrostomy/ jejunostomy feeds
1NoNoNilNoNo
2NoNoCarbamazepineYesNo
3NoNoNilNoYes
4NoYesPancreatinNoNo
5NoNoDiazoxideNoYes
6YesNoInsulinNoNo
7NoNoDiazoxideYesNo