Table 2

Published series of D−HUS, including present paper. Values are numbers of patients

ReferenceHUS (D+ and D−)D−HUS (% HUS)ESRF2-150 DeathRecurrenceFamilialComplete recovery
Milford et al 6 28815 (5)43?13/142-151
Loirat et al 8 16114 (9)61630/132-151
Imoberdorf et al 9 427 (17)2212?
Tönshoff et al 10 8921 (24)11033?
Kelles et al 11 9512 (13)12003/102-151
Wende-Fischer et al 13 6113 (21)6470?
Fitzpatrick et al 19 19220 (12)451112/192-151
Siegler et al 20 28722 (8)20428/152-151
This paper6623 (35)86625/192-151
Overall (%)1281147 (11)34 (23)33 (22)38 (26)14 (10)21/902-151 (23)
  • 2-150 ESRF = end stage renal failure.

  • 2-151 Number of patients followed up long term.