Age | dsDNA | ANA | Others | Complement | ||
---|---|---|---|---|---|---|
Patient 1 | 7 yr 8 m | Not done | Not done | IgG 22.2 g/l (7.68-11.28) | CH50:15 U/ml (25-45) | |
IgA 3.58 g/l (0.77-1.67) | C3:0.38 g/l (0.8-1.9) | |||||
IgM 0.65 g/l (0.57-2.66) | C4:0.09 g/l (0.2-0.4) | |||||
8 yr 9 m | Pos > 1000 IU/ml | IgG Pos 1/1000 H | (620 IU/ml) | pANCA neg | ||
(N < 8 U/ml) | IgM Pos 1/40 H | cANCA neg | ||||
SCAT neg (< 1/16) | ||||||
Ph latex neg (< 1/40) | ||||||
Patient 2 | 2 yr 6 m | Pos 9 IU/ml | Negative | CH50:45 U/ml (25-45) | ||
(N < 8) | C3:1.62 g/l (0.8-1.40) | |||||
C4:0.21 g/l (0.15-0.40) | ||||||
3 yr 2 m | 5 IU/ml neg | Negative | — | |||
3 yr 7 m | 25 IU/ml pos | IgG ANA Ab Pos (1/40) H | (12 IU/ml) | IgG 27.40 g/l (7.09-10.75) | ||
IgM ANA Ab Neg (1/10) | IgA 3.06 g/l (0.34-1.08) | |||||
IgM 5.68 g/l (0.42-0.80) | ||||||
3 yr 8 m | Anticardiolipin: 14 GPLU (normal 0-10) | C3:1.48 | ||||
pANCA—pos 1/64 | C4:0.19 | |||||
cANCA—neg | ||||||
3 yr 9 m | 18 IU/ml pos | IgG ANA pos 1/100 | (31 IU/ml) | Anticardiolipin 10 GPLU | CH50:38 | |
IgM ANA neg | C3:1.42 | |||||
C4:0.16 | ||||||
4 yr | 5 IU/ml neg | IgG ANA pos 1/100 | (31 IU/ml) | Anticardiolipin 6 GPLU | C3:1.25 | |
IgM ANA 1/10 | C4:0.19 | |||||
4 yr 2 m | 4 IU/ml neg | IgG ANA pos 1/80 H | (25 IU/ml) | C3:1.45 | ||
IgM ANA pos 1/20 H | C4:0.24 | |||||
4 yr 5 m | 3 IU/ml neg | IgG ANA 1/20 pos H | (6 IU/ml) | IgG 18.60 g/l (6.73-11.11) | C3:1.53 | |
IgM ANA 1/10 H | IgA 2.98 g/l (0.65-1.18) | C4:0.26 | ||||
IgM 2.78 g/l (0.36-0.70) | ||||||
4 yr 7 m | 6 IU/ml neg | IgG ANA pos 1/80 H | (25 IU/ml) | pANCA pos (1/512) | C3:1.46 | |
IgM ANA neg | cANCA neg | C4:0.29 | ||||
Antibodies to serine proteinase 3 (PR3): neg | ||||||
Antibodies to myeloperoxidase (MPO): neg |
N = normal; H = homogeneous; dsDNA = double stranded DNA; ANA = antinuclear antibodies; pANCA = perinuclear antineutrophil cytoplasmic antibody; cANCA = classical anti-neutrophil cytoplasmic antibody; GPLU = IgG phospholipid units.