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Superior mesenteric artery syndrome: a rare complication in a child with Marfan syndrome
  1. Viral Jain1,
  2. Arbinder Kumar Singal2,
  3. Chithra Ramu3,
  4. Krithiha Devi Raghunaathan4
  1. 1Department of Pediatrics, MGM University of Health Sciences, Kamothe, Navi Mumbai, Maharashtra, India
  2. 2Department of Pediatric Surgery, MGM University of Health Sciences, Kamothe & MGM's New Bombay Hospital, Vashi, Navi Mumbai, Maharashtra, India
  3. 3Department of General Surgery, PSG Institute of Medical Sciences, Coimbatore, Tamilnadu, India
  4. 4Department of Pediatrics, PSG Institute of Medical Sciences, Coimbatore, Tamilnadu, India
  1. Correspondence to Dr Arbinder Kumar Singal, Department of Pediatric Surgery, MGM University of Health Sciences, Kamothe & MGM's New Bombay Hospital, RH-5, O-26, Sector-7, Vashi, Navi Mumbai, Maharashtra 400703, India; arbinders{at}gmail.com

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A 14-year-old girl presented with sudden onset abdominal pain and distension with bilious vomiting. She had no significant prior history or weight loss. On examination, bowel sounds were normal. She was noted to have a typical marfanoid habitus with severe kyphoscoliosis (figure 1), arachnodactyly, positive thumb and wrist sign. Echocardiogram showed mitral valve prolapse, tricuspid regurgitation and normal-sized aortic root. Laboratory investigations were normal. Barium study showed dilated proximal duodenum and an abrupt cutoff near the spine …

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