Introduction According to the Ministry of Health, 3500 children are born each year with sickle cell disease in Brazil with 34.28% in Rio de Janeiro. Due to chronicity, complications and impact on the family and society, we choose to seek to know the evolving clinical features of sickle cell children seen in Petrópolis, Rio de Janeiro, Brazil.
Objective To describe the clinical and epidemiological characteristics of sickle cell anaemic children requiring hospitalisation in HEAC, Petrópolis, RJ, Brazil, in 2013.
Methodology Descriptive, retrospective, cross-sectional, quantitative study, documentary analysis of medical records of children hospitalised from January, 1 to December, 31, 2013, patients with sickle cell disease (SCD).
Results 11 patients were included and 12 hospitalizations. Diagnosis made by neonatal screening in 54.54%. Males: 63.63%. Mean age of 6.4 years (12.4y-8m) Stay hospital ranged from 3 to 10 days (mean 6 days). All mentioned earlier hospitalizations. Nutritional assessment showed 81.8% of normal weight. Reasons for hospitalizations: 50% painful crises, pneumonia, 41.66% and 16.66% splenic sequestration. Need for blood transfusions in 50% of patients and 27.27% have splenectomized. Medical monitoring irregular in 36.47% patients.
Conclusion It is known that the prognosis of SCD is variable. Appropriate monitoring, workup appropriate therapeutic approach and the events should suit purposeful action strategies to reduce complications and also minimise the consequences resulting from the disease itself. Being the HEAC solely responsible for paediatric hospitalizations in the city, this study points to the implementation of protocols and control of action aimed at better prognosis of these children.