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Cystic fibrosis presenting as kwashiorkor with florid skin rash.
  1. R J Phillips,
  2. C M Crock,
  3. M J Dillon,
  4. P T Clayton,
  5. A Curran,
  6. J I Harper
  1. Hospitals for Sick Children, London.

    Abstract

    Two infants with a florid erythematous rash and generalised oedema, hypoalbuminaemia, and anaemia were found to have cystic fibrosis. This rare presentation is associated with false negative sweat tests, delays in diagnosis, and a considerable mortality. It is proposed that this presentation represents a manifestation of kwashiorkor secondary to malabsorption. The recognition that these infants have kwashiorkor provides some insight into the pathogenesis and management of their illness.

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