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P139 A newborn with mid- aortic syndrome
  1. Yapicio&gcaron;lu Yildizdaş H1,
  2. Erdem S2,
  3. Şimşek H1,
  4. Yurdakul G3,
  5. Ece Ü3,
  6. Özlü F1,
  7. Özbarlas N2,
  8. Akçal¸ M1,
  9. Satar M1,
  10. Narli N1
  1. 1Çukurova University, Faculty of Medicine, Department of Neonatology
  2. 2Çukurova University, Faculty of Medicine, Department of Paediatric Cardiology
  3. 3Algomed Hospital, Department of Paediatrics

Abstract

Mid-aortic syndrome, a very rare condition is coarctation of abdominal aorta. It is also named as Mid-aortic dysplastic syndrome. It is characterised by segmental or generalised narrowing of either distal decending thorasic aorta or abdominal part of aorta. Some cases can be treated with transcatheteric placed stents.

40 days old infant admitted because of respiratory distress and poor sucking and hospitalised at Neonatal Intensive Care Unit with metabolic acidosis, hypertension and weak bilateral femoral pulses. Cardiomegaly was detected in chest X-ray. Ecocardiografy showed left ventricle hypertrophy but classical aort coartation could not be demonstrated although the clinic features of the patient was suggesting aortic coartation. High frequency monophasic flow was detected at abdominal aorta in doppler ultrasonography. At postnatal 47th day of the patient, angiography was performed and abdominal aorta and bilateral iliac arteries could not seen. Stent replacement or any operation were not suitable for the patient. He was exitus due to heart failure at 59th day of life.

If aortic coarctation is suspected in patient due to clinical features but is not demonstrated with ecocardiography, mid aortic syndrome must be in mind and diagnostic interventions must be performed.

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