Severe malabsorption in autoimmune polyendocrinopathy-candidosis-ectodermal dystrophy syndrome successfully treated with immunosuppression
Department of Paediatrics, Chaim Sheba Medical
Centre, Affiliated to the Tel-Aviv University, Sackler School of
Medicine, Tel Hashomer, Israel
Correspondence to: Dr S Padeh, Paediatric Department B, Chaim Sheba Medical Centre, Affiliated to the Tel-Aviv University, Sackler School of Medicine, Tel Hashomer 52621, Israel.
Accepted 2 January 1997
A 15 year old boy with autoimmune
polyendocrinopathy-candidosis-ectodermal dystrophy
syndrome suffered recurrent episodes of severe intractable
diarrhoea, steatorrhoea, and hypocalcaemia. The only treatment
modality, which controlled the malabsorption syndrome, was
immunosuppression with intravenous high dose methylprednisolone and
oral methotrexate maintenance therapy.
© 1997 by Archives of Disease in Childhood
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